Fact-sheet: Pulmonary vein stenosis


Updated on 03/26/2026 at 6:50 PM

Note : 10/10 ( 1 note )

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Definition

Stenosis of one or more pulmonary veins, which may be:

  • congenital
  • or secondary to neoplastic invasion
  • sarcoidosis
  • mediastinal fibrosis
  • atrial radiofrequency ablation
  • postsurgical

CT

Thoracic CT angiography with cardiac gating

Direct sign: caliber of one or more pulmonary veins <=6mm (normal 10-15mm)

Indirect signs:

  • Upstream lobar pulmonary edema
  • Pulmonary infarctus
  • Areas of pulmonary fibrosis
  • Decreased and delayed local pulmonary perfusion

Complications:

  • Pulmonary hypertension
  • Pneumonia
  • Hemoptysis