Fact-sheet: Kawasaki syndrome


Updated on 10/03/2018 at 2:29 PM

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Definition

Multisystemic febrile vasculitis of unknown etiology.

Population: children +++ (50% under 2 years of age and 80% under 4 years of age)

Prognosis: cardiovascular (risk of coronary aneurysm)

Clinical features

Mucocutaneous lymph node syndrome:

  • fever
  • conjunctivitis
  • polymorphic exanthema
  • oropharyngeal enanthema
  • extremity lesions
  • cervical lymphadenopathy

Cardiac involvement in 25% of cases ++: pericarditis, transient myocardiopathy with heart failure and arrhythmia, coronary or other arterial aneurysms sometimes occurring early.

Ultrasound

Abdominal Ultrasound: hydrops of the gallbladder supporting the diagnosis

TTE (1/week for 4 to 6 weeks): screening for coronary aneurysms

Management

Medical treatment: aspirin / IV immunoglobulins