Fact-sheet: Pineoblastoma - Pinealoblastoma


Updated on 08/26/2020 at 2:37 PM

Note : 0/10
Share

View all RADEOS cases associated with this fact-sheet

Definition

Malignant tumor related to PNETs (primitive neuroectodermal tumors).
Predominantly affects women under 20 years of age.

Dissemination via cerebrospinal fluid and leptomeningeal pathways is frequent.

Associations with retinoblastomas have been reported.

Clinical features

  • Rarely symptomatic.
  • Headache due to compression of the aqueduct of Sylvius
  • Behavioral disturbances

CT

  • Large lesions with ill-defined margins.
  • Rare peripheral calcifications.

MRI

  • Lesion with regular margins, lobulated, poorly defined and invasive, necrotic-cystic.
  • T1: variable signal, often hypointense.
  • T2: iso- or hypointense solid portions.
  • After gadolinium injection: heterogeneous and moderate enhancement
  • Diffusion: hyperintense solid portion
  • T2*: possible calcifications

Management

Clinical follow-up.