Fact-sheet: Osteopoikilosis - Osteopoecily
Updated on 09/17/2021 at 12:16 PM
View all RADEOS cases associated with this fact-sheet
Definition
Benign congenital condition characterized by multiple small osteosclerotic islands preferentially affecting the metaphyseal-epiphyseal regions of long bones, the pelvic and scapular girdles, and the small bones of the carpus and tarsus
Clinical features
Usually asymptomatic.
Possible associations with:
- Melorheostosis
- Palmoplantar hyperkeratosis
- Disseminated lenticular dermatofibrosis
- Focal dermal hypoplasia (Goltz-Gorlin syndrome, autosomal dominant)
Radiography
Multiple small osteosclerotic islands, round or oval, well defined, dense.
Distribution: Metaphyseal-epiphyseal regions of long bones, pelvic and scapular girdles, small bones of the carpus and tarsus.
