Fact-sheet: Papillary fibroelastoma
Updated on 08/17/2020 at 3:25 PM
View all RADEOS cases associated with this fact-sheet
Definition
Rare benign primary cardiac tumor, accounting for 10% of benign cardiac tumors and 75% of cardiac valvular tumors
Age: 60 years,
Sex ratio: 1
Valvular location:
Aortic (44%) > Mitral (35%) > Tricuspid (15%) > Pulmonary (8%)
Morphology:
Multilobulated, gelatinous, pedunculated mass
About 1 cm
Clinical features
Asymptomatic ++
Dyspnea
Stroke
Sudden death (coronary obstruction)
Ultrasound
Valvular location
Size < 15 mm
Pedunculated
Ill-defined, irregular margins
Mobility ++ (intravalvular prolapse)
CT
ECG gating
Without contrast injection:
Hypodense valvular nodule
Visible if size > 10 mm
After contrast injection:
No enhancement
Cine imaging:
Mobility +/- intravalvular prolapse
MRI
T1:
Hypointense or isointense to myocardium
Difficult to see if small in size
Valve irregularity
T2:
Hypointense or isointense to myocardium
Difficult to see if small in size
Valve irregularity
Injection:
Pseudo-nodular enhancement
Cine imaging:
Mobility/intravalvular prolapse
Differential diagnosis
Myxoma