Fact-sheet: Ecchordosis physaliphora
Updated on 08/02/2024 at 11:12 AM
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Definition
Benign congenital hamartomatous lesion derived from a notochordal remnant, typically retroclival but which may be located anywhere from the skull base to the sacrum.
Clinical features
Typically asymptomatic.
CT
Well-defined osteolytic retroclival lesion.
A bony pedicle at the base of the lesion is considered pathognomonic.
MRI
Characteristic location: retroclival, prepontine, and intradural.
Signal similar to that of CSF: hypointense on T1, hyperintense on T2, typically without enhancement after contrast administration.
Differential diagnosis
Chordoma