Fact-sheet: Ecchordosis physaliphora


Updated on 08/02/2024 at 11:12 AM

Note : 0/10

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Definition

Benign congenital hamartomatous lesion derived from a notochordal remnant, typically retroclival but which may be located anywhere from the skull base to the sacrum.

Clinical features

Typically asymptomatic.

CT

Well-defined osteolytic retroclival lesion.

A bony pedicle at the base of the lesion is considered pathognomonic.

MRI

Characteristic location: retroclival, prepontine, and intradural.

Signal similar to that of CSF: hypointense on T1, hyperintense on T2, typically without enhancement after contrast administration.

Differential diagnosis

Chordoma